Incidental Mutation 'R0991:Xrn2'
ID |
97692 |
Institutional Source |
Beutler Lab
|
Gene Symbol |
Xrn2
|
Ensembl Gene |
ENSMUSG00000027433 |
Gene Name |
5'-3' exoribonuclease 2 |
Synonyms |
|
MMRRC Submission |
039111-MU
|
Accession Numbers |
|
Essential gene? |
Probably essential
(E-score: 0.970)
|
Stock # |
R0991 (G1)
|
Quality Score |
225 |
Status
|
Not validated
|
Chromosome |
2 |
Chromosomal Location |
147012996-147078000 bp(+) (GRCm38) |
Type of Mutation |
missense |
DNA Base Change (assembly) |
A to G
at 147042082 bp (GRCm38)
|
Zygosity |
Heterozygous |
Amino Acid Change |
Lysine to Arginine
at position 587
(K587R)
|
Ref Sequence |
ENSEMBL: ENSMUSP00000028921
(fasta)
|
Gene Model |
predicted gene model for transcript(s):
[ENSMUST00000028921]
|
AlphaFold |
Q9DBR1 |
Predicted Effect |
probably benign
Transcript: ENSMUST00000028921
AA Change: K587R
PolyPhen 2
Score 0.395 (Sensitivity: 0.90; Specificity: 0.89)
|
SMART Domains |
Protein: ENSMUSP00000028921 Gene: ENSMUSG00000027433 AA Change: K587R
Domain | Start | End | E-Value | Type |
Pfam:XRN_N
|
1 |
254 |
1.5e-104 |
PFAM |
ZnF_C2HC
|
262 |
278 |
7.99e-1 |
SMART |
low complexity region
|
415 |
427 |
N/A |
INTRINSIC |
PDB:3FQD|A
|
469 |
785 |
8e-75 |
PDB |
low complexity region
|
913 |
932 |
N/A |
INTRINSIC |
|
Predicted Effect |
noncoding transcript
Transcript: ENSMUST00000136136
|
Predicted Effect |
noncoding transcript
Transcript: ENSMUST00000147057
|
Coding Region Coverage |
- 1x: 99.0%
- 3x: 97.4%
- 10x: 91.6%
- 20x: 77.4%
|
Validation Efficiency |
|
MGI Phenotype |
FUNCTION: [Summary is not available for the mouse gene. This summary is for the human ortholog.] This gene encodes a 5'-3' exonuclease that promotes transcription termination at cotranscriptional cleavage sites. Alternative splicing results in multiple transcript variants encoding different isoforms. [provided by RefSeq, Dec 2015]
|
Allele List at MGI |
|
Other mutations in this stock |
Total: 13 list
Gene | Ref | Var | Chr/Loc | Mutation | Predicted Effect | Zygosity |
Apc |
T |
A |
18: 34,316,107 |
C1985S |
probably damaging |
Het |
Atp8a2 |
T |
C |
14: 59,793,929 |
S899G |
probably benign |
Het |
Dna2 |
C |
T |
10: 62,949,187 |
R28W |
probably benign |
Het |
Dtwd1 |
G |
A |
2: 126,160,020 |
R220Q |
probably damaging |
Het |
Edil3 |
A |
T |
13: 89,289,506 |
K409* |
probably null |
Het |
Ltbp1 |
A |
G |
17: 75,225,285 |
Q118R |
possibly damaging |
Het |
Mia |
G |
A |
7: 27,180,720 |
R81C |
probably damaging |
Het |
Pik3c2a |
A |
G |
7: 116,362,045 |
|
probably null |
Het |
Prl2c2 |
G |
C |
13: 13,002,201 |
T47R |
probably damaging |
Het |
Rd3 |
A |
G |
1: 191,985,238 |
E223G |
probably damaging |
Het |
Sf3b1 |
C |
G |
1: 55,019,395 |
E12Q |
possibly damaging |
Het |
Tenm2 |
C |
T |
11: 36,063,177 |
G1236R |
possibly damaging |
Het |
Vmn1r65 |
G |
A |
7: 6,009,077 |
P53S |
probably damaging |
Het |
|
Other mutations in Xrn2 |
Allele | Source | Chr | Coord | Type | Predicted Effect | PPH Score |
IGL00158:Xrn2
|
APN |
2 |
147036750 |
missense |
probably benign |
0.00 |
IGL00950:Xrn2
|
APN |
2 |
147028146 |
nonsense |
probably null |
|
IGL01323:Xrn2
|
APN |
2 |
147034847 |
splice site |
probably benign |
|
IGL01328:Xrn2
|
APN |
2 |
147029930 |
missense |
possibly damaging |
0.90 |
IGL01545:Xrn2
|
APN |
2 |
147038179 |
missense |
probably benign |
|
IGL01729:Xrn2
|
APN |
2 |
147036797 |
critical splice donor site |
probably null |
|
IGL01805:Xrn2
|
APN |
2 |
147028143 |
missense |
probably damaging |
0.98 |
IGL02326:Xrn2
|
APN |
2 |
147047713 |
missense |
probably benign |
0.32 |
IGL02332:Xrn2
|
APN |
2 |
147026590 |
missense |
probably damaging |
1.00 |
IGL02556:Xrn2
|
APN |
2 |
147038296 |
splice site |
probably benign |
|
IGL02609:Xrn2
|
APN |
2 |
147050025 |
missense |
probably benign |
0.00 |
IGL02941:Xrn2
|
APN |
2 |
147026524 |
missense |
probably damaging |
1.00 |
IGL03119:Xrn2
|
APN |
2 |
147042872 |
missense |
probably damaging |
1.00 |
R0052:Xrn2
|
UTSW |
2 |
147040965 |
splice site |
probably benign |
|
R0114:Xrn2
|
UTSW |
2 |
147029779 |
missense |
probably damaging |
0.98 |
R0196:Xrn2
|
UTSW |
2 |
147047660 |
missense |
probably damaging |
0.99 |
R0799:Xrn2
|
UTSW |
2 |
147029898 |
missense |
probably benign |
0.03 |
R1444:Xrn2
|
UTSW |
2 |
147061488 |
missense |
probably damaging |
0.99 |
R1727:Xrn2
|
UTSW |
2 |
147061516 |
missense |
probably benign |
0.00 |
R1735:Xrn2
|
UTSW |
2 |
147061423 |
missense |
probably damaging |
1.00 |
R1885:Xrn2
|
UTSW |
2 |
147049361 |
nonsense |
probably null |
|
R2199:Xrn2
|
UTSW |
2 |
147024750 |
missense |
probably damaging |
0.96 |
R2884:Xrn2
|
UTSW |
2 |
147047656 |
missense |
probably damaging |
1.00 |
R3730:Xrn2
|
UTSW |
2 |
147024809 |
missense |
probably benign |
0.09 |
R3771:Xrn2
|
UTSW |
2 |
147061287 |
missense |
probably benign |
0.12 |
R3772:Xrn2
|
UTSW |
2 |
147061287 |
missense |
probably benign |
0.12 |
R3773:Xrn2
|
UTSW |
2 |
147061287 |
missense |
probably benign |
0.12 |
R3816:Xrn2
|
UTSW |
2 |
147028200 |
missense |
probably damaging |
1.00 |
R3927:Xrn2
|
UTSW |
2 |
147038189 |
missense |
probably benign |
|
R4173:Xrn2
|
UTSW |
2 |
147047692 |
missense |
probably damaging |
0.96 |
R4659:Xrn2
|
UTSW |
2 |
147061474 |
missense |
probably benign |
0.01 |
R4928:Xrn2
|
UTSW |
2 |
147051718 |
missense |
possibly damaging |
0.80 |
R5452:Xrn2
|
UTSW |
2 |
147024713 |
critical splice acceptor site |
probably null |
|
R5527:Xrn2
|
UTSW |
2 |
147029755 |
missense |
probably benign |
0.02 |
R6297:Xrn2
|
UTSW |
2 |
147026570 |
missense |
probably damaging |
1.00 |
R6301:Xrn2
|
UTSW |
2 |
147063342 |
missense |
probably benign |
0.05 |
R6316:Xrn2
|
UTSW |
2 |
147042010 |
missense |
probably damaging |
1.00 |
R6705:Xrn2
|
UTSW |
2 |
147036662 |
critical splice acceptor site |
probably null |
|
R7173:Xrn2
|
UTSW |
2 |
147042093 |
missense |
probably damaging |
1.00 |
R7408:Xrn2
|
UTSW |
2 |
147042097 |
critical splice donor site |
probably null |
|
R7412:Xrn2
|
UTSW |
2 |
147049346 |
missense |
probably damaging |
0.99 |
R7501:Xrn2
|
UTSW |
2 |
147029756 |
missense |
probably damaging |
1.00 |
R7856:Xrn2
|
UTSW |
2 |
147068473 |
splice site |
probably null |
|
R8912:Xrn2
|
UTSW |
2 |
147049993 |
missense |
probably benign |
0.04 |
R8969:Xrn2
|
UTSW |
2 |
147029384 |
missense |
probably damaging |
1.00 |
R9083:Xrn2
|
UTSW |
2 |
147038279 |
missense |
probably damaging |
1.00 |
R9179:Xrn2
|
UTSW |
2 |
147013161 |
missense |
probably benign |
0.04 |
Z1177:Xrn2
|
UTSW |
2 |
147028206 |
missense |
possibly damaging |
0.83 |
|
Predicted Primers |
PCR Primer
(F):5'- GTTCGCAACTACTACTGCCACCTG -3'
(R):5'- CTTCCGCCATGTTGGAGGTAGAAAG -3'
Sequencing Primer
(F):5'- TATTCGATGACAGAAGCTCTGAG -3'
(R):5'- GTAGAAAGTTACCACTTGCAGC -3'
|
Posted On |
2014-01-05 |